Extraskeletal mesenchymal chondrosarcoma of the abdomen: A rare clinical presentation

Extraskeletal mesenchymal chondrosarcoma (EMCS) is a rare malignant soft tissue tumor of chondroprogenitor cell origin. Originally, it was restricted to the bone only but that no longer case. Recent literature reports 20–33% these tumors occur at extraskeletal sites. We report one such case, in which involved anterior abdominal wall muscles and also had large intra- mass covered part peritoneal cavity. The clinical features computed tomography findings suggested diagnosis desmoid with intra-abdominal extension; however, histopathological examination immunohistochemistry proved be EMCS. case reported due dilemma diagnosis, its rarity, size, parietal, extension multiple site involvement.